LATE DIAGNOSED PHACE SYNDROME BY ANEURYSMAL SUBARACHNOID HEMORRHAGE. CASE REPORT
Abstract
PHACE syndrome is a neurocutaneous disorder coined in 1996, but the clear criteria of diagnostic were established in 2009. Even though the age of the diagnostic for the disease is during childhood, we present the case of a patient with PHACE syndrome with late diagnostic, at the age of 59-year-old by aneurysmal subarachnoid hemorrhage. The particularity of this case is represented by the paucity of the diagnostic criteria, respectively the presence of facial hemangioma and the dysplasia of the cerebral arteries at the level of Willis’s circle, associated with two aneurysms: ruptured aneurysm of the right posterior communicating artery and unruptured aneurysm of junction P1-P2 of the left posterior cerebral artery. The aim of the article is to height line the importance of early diagnostic of PHACE syndrome and the prevention of complications.
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